Successful Initiation and Maintenance of Hemodialysis in an Adult Patient with Complete Transposition of the Great Arteries

Overview

Journal Clin Exp Nephrol

Publisher Springer

Specialty Nephrology

Date 2010 Jul 8

PMID 20607578

Citations 1

Authors

Shunsuke Yamada

Hideki Yotsueda

Masatomo Taniguchi

Kazuhiko Tsuruya

Hideki Hirakata

Mitsuo Iida

Affiliations

Soon will be listed here.

Abstract

Cyanotic congenital heart disease (CCHD) is a life-threatening cardiac defect that requires palliative or corrective surgery in early life. Major advances in medical and surgical management have resulted in the survival of CCHD patients to adulthood with or without corrective surgery, though some are at risk of development of end-stage renal disease (ESRD) due to cyanotic nephropathy (CN). There is little or no information on the initiation and maintenance of hemodialysis (HD) in such patients. We present here a case of a 44-year-old man with complete transposition of the great arteries and CN-related ESRD. He had only received a bi-directional Glenn's operation and still suffered persistent severe hypoxemia and impaired cardiac function. ESRD was successfully treated with HD over more than 4 years. The case emphasizes the need for special attention in the selection and initiation of renal replacement therapy.

Citing Articles

Development of nephropathy in an adult patient after Fontan palliation for cyanotic congenital heart disease.

Hayashi K, Hashiguchi A, Ikemiyagi M, Tokuyama H, Wakino S, Itoh H CEN Case Rep. 2021; 10(3):354-358.

PMID: 33476039 PMC: 8271047. DOI: 10.1007/s13730-021-00573-2.

References

Mostafa S, Miller W, Papoutsakis E . Oxygen tension influences the differentiation, maturation and apoptosis of human megakaryocytes. Br J Haematol. 2000; 111(3):879-89. View

Hida K, Wada J, Yamasaki H, Nagake Y, Zhang H, Sugiyama H . Cyanotic congenital heart disease associated with glomerulomegaly and focal segmental glomerulosclerosis: remission of nephrotic syndrome with angiotensin converting enzyme inhibitor. Nephrol Dial Transplant. 2002; 17(1):144-7. DOI: 10.1093/ndt/17.1.144. View

Ohira S, Naito H, Amano I, Azuma N, Ikeda K, Kukita K . 2005 Japanese Society for Dialysis Therapy guidelines for vascular access construction and repair for chronic hemodialysis. Ther Apher Dial. 2006; 10(5):449-62. DOI: 10.1111/j.1744-9987.2006.00410.x. View

PERLOFF J, LATTA H, Barsotti P . Pathogenesis of the glomerular abnormality in cyanotic congenital heart disease. Am J Cardiol. 2000; 86(11):1198-204. DOI: 10.1016/s0002-9149(00)01202-9. View

Fujimoto Y, Matsushima M, Tsuzuki K, Okada M, Shibata M, Yanase Y . Nephropathy of cyanotic congenital heart disease: clinical characteristics and effectiveness of an angiotensin-converting enzyme inhibitor. Clin Nephrol. 2002; 58(2):95-102. DOI: 10.5414/cnp58095. View

Inatomi J, Matsuoka K, Fujimaru R, Nakagawa A, Iijima K . Mechanisms of development and progression of cyanotic nephropathy. Pediatr Nephrol. 2006; 21(10):1440-5. DOI: 10.1007/s00467-006-0220-5. View

Takahashi S, Ooya K, Wada N, Inagaki T, Takana Y, Saito A . Partial exchange transfusion improved renal function and proteinuria in a patient with cyanotic heart disease nephropathy. Clin Nephrol. 2003; 60(3):222-3. DOI: 10.5414/cnp60222. View

Salim M, Case C, Sade R, Watson D, Alpert B, DiSessa T . Pulmonary/systemic flow ratio in children after cavopulmonary anastomosis. J Am Coll Cardiol. 1995; 25(3):735-8. DOI: 10.1016/0735-1097(94)00441-R. View

Di Filippo S, Delahaye F, Semiond B, Celard M, Henaine R, Ninet J . Current patterns of infective endocarditis in congenital heart disease. Heart. 2006; 92(10):1490-5. PMC: 1861050. DOI: 10.1136/hrt.2005.085332. View

10.

Niwa K, Perloff J, Webb G, Murphy D, Liberthson R, Warnes C . Survey of specialized tertiary care facilities for adults with congenital heart disease. Int J Cardiol. 2004; 96(2):211-6. DOI: 10.1016/j.ijcard.2003.06.019. View

11.

Muto S, Asano Y, Hosoda S, Shionoya S, Miura Y, Urabe A . Polycythemia of end-stage renal failure: no inhibition of erythropoiesis by uremic serum and markedly increased serum erythropoietin level. Nephron. 1987; 46(1):34-6. DOI: 10.1159/000184292. View

12.

Nakanishi K, Tajima F, Osada H, Kato T, Miyazaki H, Kawai T . Thrombopoietin expression in normal and hypobaric hypoxia-induced thrombocytopenic rats. Lab Invest. 1999; 79(6):679-88. View

13.

Segall L, Covic A . Cardiovascular disease in haemodialysis and peritoneal dialysis: arguments pro haemodialysis. Nephrol Dial Transplant. 2006; 22(1):59-63. DOI: 10.1093/ndt/gfl643. View

14.

Sakazaki H, Niwa K, Echigo S, Akagi T, Nakazawa M . Predictive factors for long-term prognosis in adults with cyanotic congenital heart disease--Japanese multi-center study. Int J Cardiol. 2006; 120(1):72-8. DOI: 10.1016/j.ijcard.2006.08.081. View