Spontaneous Regression of a Terminal Myelocystocele and Associated Syringomyelia: a Case Report

Overview

Journal Childs Nerv Syst

Specialty Pediatrics

Date 2010 Feb 26

PMID 20183927

Authors

Andrew J Durnford

Roopa Mulik

Andrew D Kay

Affiliations

Soon will be listed here.

Abstract

Introduction: Terminal myelocystocele is a rare form of spinal dysraphism characterised by cystic dilatation of the central canal of a low-lying terminal cord. Typical presentation is a skin-covered dorsal mass; early surgical repair has been recommended.

Case Report: We present the case of a 4-year-old girl with a terminal myelocystocele and syrinx, which were both observed to spontaneously regress on subsequent magnetic resonance imaging.

Conclusion: Terminal myelocystocele and its associated syrinx may resolve spontaneously. Early surgical repair may not always be necessary.

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