Abnormally Thickened Papillary Muscle Resulting in Dynamic Left Ventricular Outflow Tract Obstruction: an Unusual Presentation of Hypertrophic Cardiomyopathy

Overview

Journal J Am Soc Echocardiogr

Specialty Radiology

Date 2009 Jan 10

PMID 19131012

Citations 10

Authors

Bethany A Austin

Deborah H Kwon

Nicholas G Smedira

Maran Thamilarasan

Harry M Lever

Milind Y Desai

Affiliations

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Abstract

We report the case of a symptomatic 18-year-old patient, gene-positive for hypertrophic cardiomyopathy (HCM), who presented with symptomatic dynamic left ventricular outflow tract (LVOT) obstruction caused by an abnormally thickened papillary muscle in the absence of septal hypertrophy. This was confirmed using multimodality imaging, including echocardiography and magnetic resonance imaging. He successfully underwent surgery for papillary muscle realignment without septal myectomy.

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