Carney's Triad: Case Report and Review

Overview

Journal J Gastrointest Cancer

Publisher Springer

Specialties Gastroenterology
Oncology

Date 2008 Dec 18

PMID 19089668

Citations 1

Authors

R Diaz Nieto

A Arjona Sanchez

M Gomez Alvarez

D Martinez Cecilia

J M Sanchez Hidalgo

R Ciria Bru

M C Perez Manrique

J Sanchez Rodriguez

S Rufian Pena

Affiliations

Soon will be listed here.

Abstract

Introduction: Carney's triad is a rare pathogenic entity which consists of the association in young women of multiple condromatosis in the lung, gastric leiomyosarcoma, and extradrenal paraganglioma; although the presence of three at the same time is not required for its diagnosis.

Case Report: We present the case of a 27-year-old woman who was diagnosed of pulmonary multiple hamartomatosis and gastric stromal tumor.

Discussion: A review of the literature shows the most important prognosis factors and therapeutic options. Surgery for gastrointestinal stromal tumors and extradrenal paraganglioma seems to be the best treatment up to date.

Citing Articles

Gastric Gist with Syncronous Ampullary Gangliocytic Paraganglyoma: A Novel Presentation of an Incomplete Carney's Triad.

Juarez-Parra M, Guzman-Huerta E, Ochoa-Rodriguez G, Limon-Rodriguez J, Zamudio-Vazquez Z, Osoria-Alba L J Gastrointest Cancer. 2015; 46(3):317-21.

PMID: 25859840 DOI: 10.1007/s12029-015-9717-0.

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