Severe Nephropathy in Three Adolescents with Cystic Fibrosis

Overview

Journal Arch Dis Child

Specialty Pediatrics

Date 1991 Dec 1

PMID 1776895

Citations 7

Authors

M L Melzi

D Costantini

M Giani

A C Appiani

A M Giunta

Affiliations

Soon will be listed here.

Abstract

Renal involvement has rarely been reported in patients with cystic fibrosis. We describe severe nephropathy with a rapidly fatal outcome in three adolescents with cystic fibrosis, and evaluate the important repercussions that the nephrotic syndrome had on the precarious clinical situation of these patients.

Citing Articles

Clinicopathologic Features of Kidney Disease in Patients With Cystic Fibrosis.

Caza T, Walker P Kidney Int Rep. 2024; 9(7):2286-2289.

PMID: 39081754 PMC: 11284363. DOI: 10.1016/j.ekir.2024.04.044.

Cystic fibrosis of pancreas and nephrotic syndrome: a rare association.

Kelekci S, Karabel M, Ece A, Sen V, Gunes A, Yolbas I Korean J Pediatr. 2013; 56(10):456-8.

PMID: 24244215 PMC: 3827495. DOI: 10.3345/kjp.2013.56.10.456.

Cadmium regulates the expression of the CFTR chloride channel in human airway epithelial cells.

Rennolds J, Butler S, Maloney K, Boyaka P, Davis I, Knoell D Toxicol Sci. 2010; 116(1):349-58.

PMID: 20363832 PMC: 2886859. DOI: 10.1093/toxsci/kfq101.

Renal involvement in cystic fibrosis: diseases spectrum and clinical relevance.

Yahiaoui Y, Jablonski M, Hubert D, Mosnier-Pudar H, Noel L, Stern M Clin J Am Soc Nephrol. 2009; 4(5):921-8.

PMID: 19406970 PMC: 2676191. DOI: 10.2215/CJN.00750209.

Cystic fibrosis and renal disease: a case report.

Al-Shawwa B, Rao A J Med Case Rep. 2007; 1:24.

PMID: 17547751 PMC: 1896172. DOI: 10.1186/1752-1947-1-24.

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