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[The Use of Nd-Yag Laser in the Treatment of Tracheal Tumor in 14 Years Old Child with Mukopolisacharydosis Type II]

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Journal Otolaryngol Pol
Date 2006 Dec 13
PMID 17152817
Citations 2
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Abstract

Hunter's Syndrome (MPS II) is a class of hereditary disorder characterized by a deficiency of specific enzyme--iduronate sulphatase required to break down mucopolisacharides and occurs in Poland in one of 100-150 thousand male live births. MPS II may be lethal in the second decade of life as a result of infiltrativ cardiomiopathy leading to irreversible heart failure or upper airway obstruction caused by infiltration, granulation and deformation in trachea or larynx. We report a case of 14-year-old male with Hunter Syndrome who developed tracheal obstruction and was treated with Nd-Yag laser. We discuss the possibility of treatment and our results--improvement in patient's symptomatic and functional status.

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