Absent Right and Persistent Left Superior Vena Cava: Fetal and Neonatal Echocardiographic Diagnosis

Overview

Journal Pediatr Cardiol

Specialties Cardiology & Vascular Diseases
Pediatrics

Date 2006 Aug 26

PMID 16933072

Citations 4

Authors

G Favia Guarnieri

F Romano

L Clerico

G Balducci

Affiliations

Soon will be listed here.

Abstract

Absence of the right superior vena cava (SVC) is a rare event occurring in patients without congenital cardiovascular abnormalities. Since absence of the right SVC is usually clinically silent, its diagnosis is mandatory prior to invasive medical or surgical procedures. We report two cases of echocardiographic diagnosis of absence of the right SVC with persistent left SVC and a large coronary sinus in structurally normal heart in a fetus of 20 weeks' gestation and in a newborn. The diagnosis was confirmed by transthoracic contrast echocardiography with intravenous injection of agitated saline into the right arm.

Citing Articles

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Persistent right superior vena cava in a patient with dextrocardia: Case report and review of the literature.

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Prenatal diagnosis of persistent left and absent right superior vena cava.

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Prenatal diagnosis of persistent left superior vena cava and its clinical significance.

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