Upper Airways Abnormalities and Tracheal Problems in Morquio's Disease

Overview

Journal Thorax

Date 2003 May 3

PMID 12728175

Citations 24

Authors

P P WALKER

E Rose

J G Williams

Affiliations

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Abstract

Morquio's disease is a metabolic disorder that can cause various respiratory abnormalities. Patients who live into adulthood are likely to develop upper airway problems and respiratory failure. With advances in home ventilation, these patients are increasingly likely to be referred to specialist respiratory units. We describe our experiences with two such patients.

Citing Articles

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Tracheal Narrowing and Its Impact on Anesthesia Care in Patients With Morquio A (Mucopolysaccharidosis Type IVA): An Observational Study.

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Tracheal Resection for Critical Airway Obstruction in Morquio A Syndrome.

Frauenfelder C, Maughan E, Kenth J, Nandi R, Jones S, Walker R Case Rep Pediatr. 2023; 2023:7976780.

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Tracheal narrowing in children and adults with mucopolysaccharidosis type IVA: evaluation with computed tomography angiography.

Averill L, Kecskemethy H, Theroux M, Mackenzie W, Pizarro C, Bober M Pediatr Radiol. 2021; 51(7):1202-1213.

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