N-Dicarboxylmonoglycines: Excretion in Dicarboxylic Acidurias and Mode of Formation

Overview

Journal J Inherit Metab Dis

Publisher Wiley

Date 1978 Jan 1

PMID 116078

Authors

I H Gron

N Gregersen

K Rasmussen

Affiliations

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References

Tanaka K, Isselbacher K . The isolation and identification of N-isovalerylglycine from urine of patients with isovaleric acidemia. J Biol Chem. 1967; 242(12):2966-72. View

Bartlett K, GOMPERTZ D . The specificity of glycine-N-acylase and acylglycine excretion in the organicacidaemias. Biochem Med. 1974; 10(1):15-23. DOI: 10.1016/0006-2944(74)90004-0. View

Gregersen N, Gron I, Rasmussen K, Kolvraa S . Gas chromatographic mass spectrometric identification of N-dicarboxylmonoglycines. Biomed Mass Spectrom. 1978; 5(1):80-3. DOI: 10.1002/bms.1200050115. View

Rasmussen K, Ando T, Nyhan W, Hull D, Cottom D, Kilroy A . Excretion of tiglylglycine in propionic acidemia. J Pediatr. 1972; 81(5):970-2. DOI: 10.1016/s0022-3476(72)80551-1. View

GOMPERTZ D, Draffan G, Watts J, Hull D . Biotin-responsive beta-methylcrotonylglycinuria. Lancet. 1971; 2(7714):22-4. DOI: 10.1016/s0140-6736(71)90009-2. View