Fibrosing Alveolitis Predating Microscopic Polyangiitis

Overview

Journal Scand J Rheumatol

Publisher Informa Healthcare

Specialty Rheumatology

Date 1999 Sep 30

PMID 10503564

Citations 8

Authors

A Becker-Merok

J C Nossent

N Ritland

Affiliations

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Abstract

A 65 year old male was diagnosed with "cryptogenic fibrosing alveolitis (CFA)" and treated successfully with Prednisone. In the year following Prednisone-tapering he presented with livedo reticularis, segmental pauci-immune glomerulonephritis and necrotizing vasculitis of the peripheral nerves, increased pulmonary fibrosis, and the presence of p-ANCA antibodies. Aggressive immunosuppressive treatment of this microscopic polyangiitis (MPA) was successful and also resulted in stabilization of the pulmonary fibrosis. This case illustrates that MPA may present itself monosymptomatic as CFA.

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